MovDisordV3, Main, Exploration, bibRecord, 002A58

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Identifieur interne : 002A58 ( Main/Exploration ); précédent : 002A57; suivant : 002A59

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Auteurs : Gian Luca Fomi [Italie] ; Manuela Balocco [Italie] ; Laura Cremonesi [Italie] ; Giovanni Abbruzzese [Italie] ; Roberto Carlo Parodi [Italie] ; Roberta Marchese [Italie]

Source :

Movement disorders [ 0885-3185 ] ; 2008.

RBID : Pascal:08-0251877

Descripteurs français

Pascal (Inist)
- Pathologie du système nerveux, Fer, Traitement, Encéphale, Défériprone.
Wicri :
- topic : Fer.

English descriptors

KwdEn :
- Deferiprone, Encephalon, Iron, Nervous system diseases, Treatment.

Abstract

We report the results of iron chelating treatment with deferiprone in a 61-year-old woman with signs and symptoms of neurodegeneration with brain iron accumulation (NBIA). After 6 months of therapy the patient's gait had improved and a reduction in the incidence of choreic dyskinesias was observed. Her gait returned to normal after an additional 2 months of therapy, at which time there was a further reduction in involuntary movements and a partial resolution of the blepharospasm.

Affiliations:

Links toward previous steps (curation, corpus...)

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Le document en format XML

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<front><div type="abstract" xml:lang="en">We report the results of iron chelating treatment with deferiprone in a 61-year-old woman with signs and symptoms of neurodegeneration with brain iron accumulation (NBIA). After 6 months of therapy the patient's gait had improved and a reduction in the incidence of choreic dyskinesias was observed. Her gait returned to normal after an additional 2 months of therapy, at which time there was a further reduction in involuntary movements and a partial resolution of the blepharospasm.</div>
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	Movement Disorders (revue)
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Movement Disorders (revue)

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Regression of Symptoms After Selective Iron Chelation Therapy in a Case of Neurodegeneration with Brain Iron Accumulation

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri